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Abstract:

Acardiac fetus («acardiac monster», «acardiac vampire») - is rarely encountered pathology of pregnancy in which one of monochorionic fetuses (recipient) is formless mass, with absence of the heart and some internal organs, life and growth of which is related to parasitism on other fetus.

The main reason for the formation of this defect is an abnormal location of placental vessels ir monochorionic twins. Characteristic are the underdevelopment of the upper body of the recipient fetus (underdevelopment of the upper part of chest, the absence of heart or the presence of rudimentary heart) and acephaly

The article presents results of the analysis of the world literature data, and given own observation of acardiac fetus stillborn.

We specify frequency causes, as well as the clinical and morphological features such anomalies. Possibilities of the post-mortem magnetic resonance and computed tomography imaging in determining the type of acardiac fetus. According to results of the analysis, it was the most efficient construction and analysis of volumetric reconstruction of bone tissues.

Conclusion: post-mortem CT and MRI are advisable in some cases as a complement to the postmortem examination.

 

References

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Abstract:

We analyzed literature data and demonstrate own clinical case of stillborn with prune belly syndrome. Development of prune belly syndrome is a rare but severe pathology of the fetus. We have indicated the frequency, causes of development and also clinical and morphological features of this anomaly, including in combination with the cloaca. Noted that such families need genetic testing due to the high of redevelopment of similar anomalies. We showed possibilities of postmortem computed tomography in identifying concomitant pathology, including three dimensional reconstruction of bone tissue. It was concluded that carrying out postmortem CT as complement to the autopsy is expedient.

 

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